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A case of Mayer-Rokitansky-Kuster- Hauser syndrome type I

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Case Report

Author Details : Akanksha Sanjay Chandekar*, Sushma Rakesh Shah, Monica George, Riya Vaghela

Volume : 11, Issue : 2, Year : 2024

Article Page : 301-303

https://doi.org/10.18231/j.ijogr.2024.057

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Abstract

Rokitansky-Kuster-Hauser (MRKH) syndrome is a rare congenital disorder characterised by absence of uterus and vagina. Ovaries and fallopian tubes are normal and functional. Its incidence is 1 in 4500-5000 female. Patients present with primary amenorrhea with normal external genitalia and development of secondary sexual characteristics, and 46XX karyotype. It is usually diagnosed by MRI, CT or transabdominal USG, with MRI being the gold standard.
 

Keywords: Mullerian agenesis, MRKH syndrome, Primary amenorrhea, Dyspareunia, Davydov, Vaginoplasty.

How to cite : Chandekar A S, Shah S R, George M, Vaghela R, A case of Mayer-Rokitansky-Kuster- Hauser syndrome type I. Indian J Obstet Gynecol Res 2024;11(2):301-303

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