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The sequence of acrania–exencephaly–anencephaly (AEAS)- An infrequent case report

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Case Report

Author Details : Heera Trivikrama Shenoy*, Najah Ismail Kunju, Naseemabeevi Ahmed Khan, Sudhya P Puthanayil, Sangeetha Ambujakshan Ambujakshan

Volume : 11, Issue : 2, Year : 2024

Article Page : 304-307

https://doi.org/10.18231/j.ijogr.2024.058

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Abstract

Acrania–exencephaly–anencephaly sequence has an incidence of 3.6–5.4 for 10,000 live births and has been reported in literature. Exencephaly, described here is a defect of the neural tube which occurs due to the absence of closure of the neural fold. The main diagnostic ultrasound features include that are characterized by acrania, decreased size of cranial pole in comparison with the chest, irregular cranial surface, with increased amniotic fluid echogenicity due to the damaged brain tissue. Associated with amniotic band syndrome, Pentalogy of Cantrell, limb anomalies and ventral body wall defects. It is incompatible with life. Conducting programs training the budding neuro-sonographers about the knowledge in detection, diagnosis of NTD according to the Carnegie Classification is crucial to look forward in pathogenesis and application in the clinical scenario.
 

Keywords: Acrania, Ultrasound, Anomaly, Brain defect, Exencephaly.

How to cite : Shenoy H T, Kunju N I, Khan N A, Puthanayil S P, Ambujakshan S A, The sequence of acrania–exencephaly–anencephaly (AEAS)- An infrequent case report. Indian J Obstet Gynecol Res 2024;11(2):304-307

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